Biliary Atresia
Mostrando 25-36 de 42 artigos, teses e dissertações.
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25. Utilization of sialic acid as a coreceptor is required for reovirus-induced biliary disease
Infection of neonatal mice with some reovirus strains produces a disease similar to infantile biliary atresia, but previous attempts to correlate reovirus infection with this disease have yielded conflicting results. We used isogenic reovirus strains T3SA– and T3SA+, which differ solely in the capacity to bind sialic acid as a coreceptor, to define the rol
American Society for Clinical Investigation.
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26. Extrahepatic Biliary Atresia
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27. Maternal microchimerism in the livers of patients with Biliary atresia
BioMed Central.
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28. Current management of biliary atresia
Extra‐hepatic biliary atresia occurs in approximately 1:15 000 live births leading to about 50 new cases/year in the UK. Presentation is with prolonged jaundice, usually in a term baby who develops signs of obstructive jaundice. Management has been improved by public and professional education to encourage early referral and diagnosis to facilitate initi
BMJ Group.
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29. Portal lymphadenopathy associated with lipofuscin in chronic cholestatic liver disease.
To determine whether portal lymphadenopathy in primary biliary cirrhosis is caused by deposition of lipofuscin pigment in sinus histiocytes and to compare primary biliary cirrhosis with other liver diseases a retrospective study on a consecutive series of 169 livers obtained at transplantation was carried out. There were grouped into eight diagnostic categor
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30. Evaluation, operative management, and outcome after liver transplantation in children with biliary atresia and situs inversus.
INTRODUCTION: Biliary atresia, a common indication for liver transplantation, can be associated with situs inversus. Our experience with liver transplantation in children (n = 6) was reviewed retrospectively. PATIENTS AND METHODS: Preoperative duplex sonography, computerized tomography, and visceral angiography were obtained. Vascular anomalies identified in
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31. Asplenia and polysplenia syndromes with abnormalities of lateralisation in a sibship.
In the family presented here the first child had asplenia syndrome with cor biloculare' transposition of the great vessels, pulmonary stenosis, and anomalous pulmonary venous drainage. Another sib had situs inversus with polysplenia syndrome, including very similar cardiovascular defects and biliary atresia. The possibility that these two syndromes, namely a
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32. Hepatic hypertrophic osteoarthropathy and liver transplantation.
OBJECTIVES--To document the variety of liver diseases and the clinical picture of hepatic hypertrophic osteoarthropathy (HOA) complicated by arthritis and to report the effects of successful liver transplantation on this disabling condition. METHODS--Seven patients with severe liver disease (two biliary atresia, two primary sclerosing cholangitis, one Wilson
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33. Biliary atresia-polysplenia syndrome: surgical and clinical relevance in liver transplantation.
OBJECTIVE: To review a single center's 10-year experience with liver transplantation (LTx) for the biliary atresia-polysplenia syndrome (BA-PS) and to define surgical and clinical guidelines for its management. SUMMARY BACKGROUND DATA: BA is the most common indication for pediatric liver transplantation (LTx) and is associated with PS in 12% of cases. Only a
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34. Living related liver transplantation in adults.
OBJECTIVE: To evaluate the outcome of living related liver transplantation (LRLT) in adult patients and to assess graft size disparity and graft regeneration. SUMMARY BACKGROUND DATA: Although LRLT has been accepted as an optional life-saving procedure for pediatric patients with end-stage liver disease, the feasibility of LRLT for adult patients has not bee
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35. Primary ciliary dyskinesia: current state of the art
Primary ciliary dyskinesia (PCD) is usually inherited as an autosomal recessive disorder and presents with upper and lower respiratory tract infection, and mirror image arrangement in around 50% of cases. Cilia dysfunction is also implicated in a wider spectrum of disease, including polycystic liver and kidney disease, central nervous system problems includi
BMJ Group.
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36. Keratin 8 and 18 mutations are risk factors for developing liver disease of multiple etiologies
Keratin 8 and 18 (K8/K18) mutations are found in patients with cryptogenic cirrhosis, but the role of keratin mutations in noncryptogenic cirrhosis and the incidence of keratin mutations in the general population are not known. We screened for K8/K18 mutations in genomic DNA isolated from 314 liver explants of patients who primarily had noncryptogenic cirrho
The National Academy of Sciences.