Biliary Atresia
Mostrando 1-12 de 42 artigos, teses e dissertações.
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1. Abnormalities of Cardiac Situs and Heart Disease Diagnosed by Echocardiography in Patients with Biliary Atresia
Abstract Background: Left isomerism (LI) is a common finding in patients with biliary atresia (BA), and it can be identified by echocardiography. Several comorbidities may be present in patients with LI, including heart disease. Objective: To investigate the prevalence of LI and heart disease in children (< 18 years of age) with BA followed-up at Hospital
International Journal of Cardiovascular Sciences. Publicado em: 2022
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2. Histological evolution of fibrosis in patients with biliary atresia
RESUMO Objetivo: Avaliar a evolução dos achados histológicos de pacientes com atresia biliar (AB), enfatizando a progressão da fibrose e comparando a biópsia hepática diagnóstica (BHD) com a biópsia hepática cirúrgica (BHC), realizada durante a portoenterostomia de Kasai. Método: Estudo retrospectivo com 51 pacientes portadores de AB submetidos
J. Bras. Patol. Med. Lab.. Publicado em: 11/11/2019
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3. MULTIVARIATE ANALYSIS OF BILIARY FLOW-RELATED FACTORS AND POST-KASAI SURVIVAL IN BILIARY ATRESIA PATIENTS
RESUMO CONTEXTO: A atresia biliar representa a principal causa de colestase tratada cirurgicamente durante o período neonatal. Se a criança não for operada, ela evolui invariavelmente para cirrose biliar secundária. OBJETIVO: Avaliar, através de análise multivariada, os fatores prognósticos associados à presença de fluxo biliar e à sobrevida co
Arq. Gastroenterol.. Publicado em: 20/05/2019
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4. Current management of biliary atresia based on 35 years of experience at a single center
OBJECTIVE: The prognosis of patients with biliary atresia undergoing Kasai portoenterostomy is related to the timing of the diagnosis and the indication for the procedure. The purpose of the present study is to present a practical flowchart based on 257 children who underwent Kasai portoenterostomy. METHODS: We conducted a retrospective cohort study of pat
Clinics. Publicado em: 10/07/2018
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5. Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful sur
Braz J Med Biol Res. Publicado em: 02/02/2016
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6. Dynamic expression of desmin, α-SMA and TGF-β1 during hepatic fibrogenesis induced by selective bile duct ligation in young rats
We previously described a selective bile duct ligation model to elucidate the process of hepatic fibrogenesis in children with biliary atresia or intrahepatic biliary stenosis. Using this model, we identified changes in the expression of alpha smooth muscle actin (α-SMA) both in the obstructed parenchyma and in the hepatic parenchyma adjacent to the obstruc
Braz J Med Biol Res. Publicado em: 15/08/2014
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7. Advances in biliary atresia : from patient care to research
Biliary atresia, the most common cause of liver transplantation in children, remains a challenge for clinicians and investigators. The development of new therapeutic options, besides the typical hepatoportoenterostomy, depends on a greater understanding of its pathogenesis and how it relates to the clinical phenotypes at diagnosis and the rate of disease pro
Publicado em: 2011
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8. Advances in biliary atresia: from patient care to research
Biliary atresia, the most common cause of liver transplantation in children, remains a challenge for clinicians and investigators. The development of new therapeutic options, besides the typical hepatoportoenterostomy, depends on a greater understanding of its pathogenesis and how it relates to the clinical phenotypes at diagnosis and the rate of disease pro
Brazilian Journal of Medical and Biological Research. Publicado em: 2010-06
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9. Avaliação quantitativa de vegf a por qrt-pcr em fígados de pacientes com atresia biliar
A Atresia Biliar, principal causa de transplante hepático em crianças, tem causa obscura. Para avaliar a presença de uma arteriopatia como causa da doença investigamos a expressão do vascular endothelial growth factor A (VEGF A) em fígados de pacientes afetados. Amostras de fígados de pacientes com Atresia Biliar (n=21) e controles com outras causas d
Publicado em: 2010
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10. Histopathological diagnosis of intra- and extrahepatic neonatal cholestasis
The histopathology of the liver is fundamental for the differential diagnosis between intra- and extrahepatic causes of neonatal cholestasis. However, histopathological findings may overlap and there is disagreement among authors concerning those which could discriminate between intra- and extrahepatic cholestasis. Forty-six liver biopsies (35 wedge biopsies
Publicado em: 2010
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11. Avaliação da expressão dos fatores angiogênicos VEGF a e seus receptores e FGFB em tecido hepático de pacientes com atresia biliar
A atresia biliar (AB) é uma colangiopatia de etiologia indeterminada que leva à necessidade de transplante hepático, mesmo com a realização da Portoenterostomia em tempo hábil. O espessamento da camada média da artéria hepática sugere o envolvimento de um distúrbio angiogênico. Este estudo objetivou avaliar a expressão imunoistoquímica do VEGF A
IBICT - Instituto Brasileiro de Informação em Ciência e Tecnologia. Publicado em: 2009
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12. Niveis sericos das vitaminas lipossoluveis (A, D e E) em pacientes com atresia biliar e hepatite auto-imune e a relação com o estado nutricional e indicadores clinicos e laboratoriais / Serum levels of fat-soluble vitamins (A, D and E) in patientes with biliary atresia and auto-immune hepatitis and relations with the nutritional status and clinic and laboratorial indicators
The chronic liver diseases can cause malabsorption of lipids and fat-soluble vitamins, leading to a deficient nutritional status. The aim of research was: to evaluate the relation between serum levels of fat-soluble vitamins (A, D and E) on chidren and adolescents with biliary atresia (BA) and auto-immune hepatitis (AIH) with the nutritional status and with
Publicado em: 2008