Síndrome de Peutz-Jeghers: relato de caso
AUTOR(ES)
Andrade, Aderivaldo Coelho de, Carvalho Júnior, Edílson, Dantas, Karoline da Silva, Sousa, Jocerlano Santos de, Morais, Ricardo Keyson Paiva de
FONTE
Revista do Colégio Brasileiro de Cirurgiões
DATA DE PUBLICAÇÃO
2008-06
RESUMO
Peutz-Jeghers syndrome (PJS) is a dominant autosomal inherited disorder characterized by intestinal hamartomatous polyps in association with mucocutaneous melanocytic maculae. This syndrome is rare, and the frequency reaches from 1 in 60,000 to 1 in 300,000 people in the USA. The symptom presentations vary greatly in this disease. Some patients require minor clinical treatment while others undergo many hospitalizations and surgical treatments. In addition, patients with PJS have an increased risk for developing a variety of malignant tumors. The aim of the present study was to report one case studied of Peutz-Jeghers syndrome.
