Primary localized cutaneous amyloidosis with lichen and poikiloderma-like lesions and an excellent response to systemic acitretin

AUTOR(ES)

MA, Han, Su, Xiangyang, Zhu, Guoxing, Yin, Songchao, Lu, Chun, Lai, Wei

FONTE

An. Bras. Dermatol.

DATA DE PUBLICAÇÃO

2016-10

RESUMO

Abstract: Primary localized cutaneous amyloidosis is a skin-limited amyloidosis that does not involve internal organs. It is clinically subclassified into 3 general categories and some rare variants. However, there is considerable overlap within the classification. Though there are a variety of therapeutic measures, the treatment is often unsatisfactory, particularly when the disease is severe and extensive. We describe a rare case of primary localized cutaneous amyloidosis with lichen and poikiloderma-like lesions that showed an excellent response to systemic acitretin.

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