Neurological crisis in hereditary tyrosinaemia and complete reversal after liver transplantation.

AUTOR(ES)

Noble-Jamieson, G

RESUMO

A 19 month old Indian girl with tyrosinaemia developed a severe generalised neuropathy involving both phrenic nerves. Treatment with haemarginate failed to improve her condition. After liver transplantation the raised concentrations of the neurotoxin delta amino-laevulinic acid returned to normal and gradual but complete neurological recovery occurred over a period of 13 months.

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