Disc oedema in association with Hunter's syndrome: ocular histopathological findings.

AUTOR(ES)

Beck, M

RESUMO

The histopathology of the posterior half of one eye and the optic nerves of a man with Hunter's syndrome, who was known to have disc oedema without raised intracranial pressure for 11 years of his life, is reported. The possible pathogenesis of the disc oedema is discussed; an important contributory factor was the deposition of abnormal mucopolysaccharides within the sclera. This caused gross thickening of the sclera with compression of the optic nerve at the intrascleral level.

Documentos Relacionados

• Papilloedema in association with Hunter's syndrome.
• Bloom's syndrome: a probable new case with cytogenetic findings.
• Visual vertigo syndrome: clinical and posturography findings.
• Neurogenic bladder in Hunter's syndrome.
• Segregation and sporadic cases in families with Hunter's syndrome.