Central motor and sensory conduction in X-linked recessive bulbospinal neuronopathy.
AUTOR(ES)
Kachi, T
RESUMO
Central conduction was studied in 12 patients with X-linked recessive bulbospinal neuronopathy (XBSN) using percutaneous electrical cortical, cervical and lumbar stimulation and somatosensory evoked potentials (SEPs). The central motor conduction time from the motor cortex to the cervical and lumbar segments of the spinal cord was normal in XBSN. SEPs, however, were abnormal or central sensory conduction time was prolonged in patients with XBSN. These results are consistent with the clinicopathological findings of XBSN in which the primary sensory neurons are involved as well as the lower motor neurons in the CNS, whereas the upper motor neurons are well preserved.
ACESSO AO ARTIGO
http://www.pubmedcentral.nih.gov/articlerender.fcgi?artid=489083Documentos Relacionados
- X-linked recessive bulbospinal neuronopathy: a report of ten cases.
- X-linked bulbo-spinal neuronopathy: a family study of three patients.
- Very late onset X-linked recessive bulbospinal neuronopathy: mild clinical features and a mild increase in the size of tandem CAG repeat in androgen receptor gene.
- An hereditary sensory and autonomic neuropathy transmitted as an X-linked recessive trait.
- Sandhoff disease mimicking adult-onset bulbospinal neuronopathy.