Structural and functional aspects in Möbius syndrome children: a speech therapy view / Aspectos estruturais e funcionais em crianças portadoras da seqüência de Möbius: uma visão fonoaudiológica

AUTOR(ES)
DATA DE PUBLICAÇÃO

2009

RESUMO

The aim of this study was to evaluate MS oral miofunctional system and stomatognathic functions in order to define MS phonoaudiological structural phenotype and correlate any changes with the affected anatomical structures, aiming at preparing a standard of care program targeted to MS. Thirty-one male and female patients aged 4 to 16 years old were examined as outpatients of clinical follow-up at Neuropediatrics Department of HC FMUSP Instituto da Criança. Patients with nasogastric or gastrostomy tube and/or who were mentally disabled were excluded. Results showed 24 patients with half-open lips and 29 with altered mobility. For 24 patients at rest, tongue was on the floor of the mouth, 6 on the papilla and 1 between the teeth. Tongue mobility revealed alterations in 51.6% of the cases. Seventy-seven per cent of the patients had ogival palate and 77% had asymmetric chicks. Mandible with reduced opening was found in 55% and mentalis muscle (at rest) was normal in 71% of the cases. For most patients chewing and phonation changes were observed, and 74% had nasal respiration; 27 patients had efficient sucking and 13 had normal swallowing. It was found that the most affected orofacial structures were lips, due to VII nerve palsy, more precisely of zigomatic and upper and lower buccal branches; some cases also showed alterations of chewing and tongue mobility, V and XII nerves. The phonoaudiological treatment should target facial musculature and phonoarticulatory organs stimulation and suiting functions or made them viable, adapted to the clinical picture.

ASSUNTO(S)

paralisia facial facial palsy fonoaudiologia speech therapy möbius syndrome síndrome de möbius

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